missing translation for 'onlineSavingsMsg'
Learn More
Learn More
HMBS Rabbit anti-Human, Mouse, Rat, Polyclonal, Proteintech
Rabbit Polyclonal Antibody
1696.32 NOK - 4796.50 NOK
Specifications
| Antigen | HMBS |
|---|---|
| Concentration | 0.2 mg/mL |
| Applications | Immunocytochemistry, Western Blot, Immunoprecipitation, Immunofluorescence |
| Classification | Polyclonal |
| Conjugate | Unconjugated |
| Product Code | Brand | Quantity | Price | Quantity & Availability | |||||
|---|---|---|---|---|---|---|---|---|---|
| Product Code | Brand | Quantity | Price | Quantity & Availability | |||||
|
16803624
|
Proteintech
14797-1-AP-20UL |
20 μL |
1696.32 NOK
20µL |
Please sign in to purchase this item. Need a web account? Register with us today! | |||||
|
16893614
|
Proteintech
14797-1-AP-150UL |
150 μL |
4796.50 NOK
150µL |
Please sign in to purchase this item. Need a web account? Register with us today! | |||||
Description
PBGD (porphobilinogen deaminase), also designated hydroxymethylbilane synthase, is a cytoplasmic enzyme found in the heme synthesis pathway. PBGD belongs to the HMBS (hydroxymethylbilane synthase) family. Deficiency of PBGD causes errors in pyrrole metabolism, which in turn leads to an inherited autosomal disorder called acute intermittent porphyria (AIP). AIP is characterized by acute attacks of neurological dysfunctions with hypertension, tachycardia, peripheral neurologic disturbances, abdominal pain and excessive amounts of aminolevulinic acid and porphobilinogen in the urine.Specifications
| HMBS | |
| Immunocytochemistry, Western Blot, Immunoprecipitation, Immunofluorescence | |
| Unconjugated | |
| Rabbit | |
| Mouse, Rat, Human | |
| P08397, P19356, P22907 | |
| 15288, 25709, 3145 | |
| HMBS Fusion Protein Ag6509 | |
| Primary | |
| -20°C | |
| HMBS |
| 0.2 mg/mL | |
| Polyclonal | |
| Liquid | |
| RUO | |
| PBS with 50% glycerol and 0.02% sodium azide; pH 7.3 | |
| HMBS, hydroxymethylbilane synthase, PBG D, PBGD, Porphobilinogen deaminase, Pre uroporphyrinogen synthase, UPS | |
| Hmbs | |
| IgG | |
| Antigen Affinity Chromatography | |
| Antibody |
Spot an opportunity for improvement?Share a Content Correction
Product Content Correction
Your input is important to us. Please complete this form to provide feedback related to the content on this product.
Product Title